Double outlet right ventricle

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Double outlet right ventricle
PMC4316658 13023 2014 144 Fig2 HTML (1).png
Double outlet right ventricle sectioned in four-chamber fashion, showing the aorta arising exclusively from the right ventricle

Double outlet right ventricle (DORV) is a form of congenital heart disease where both of the great arteries connect (in whole or in part) to the right ventricle (RV). In some cases it is found that this occurs on the left side of the heart rather than the right side.

DORV affects between 1% and 3% of people born with congenital heart defects.[1]

Signs and symptoms

Clinical features include a heart murmur and rapid heartbeat.[2]


DORV occurs in multiple forms, with variability of great artery position and size, as well as of ventricular septal defect (VSD) location. It can occur with or without transposition of the great arteries. The clinical manifestations are similarly variable, depending on how the anatomical defects affect the physiology of the heart, in terms of altering the normal flow of blood from the RV and left ventricle (LV) to the aorta and pulmonary artery. For example:[citation needed]


Diagnosis is by medical imaging; chest X-ray, echocardiogram, MRI.[2]


DORV is treated with surgery.[citation needed]


DORV affects between 1% and 3% of people born with congenital heart defects.[1]

Chromosomal abnormalities were reported in about 40% of reported cases in the medical literature.[1]


  1. 1.0 1.1 1.2 Obler D, Juraszek AL, Smoot LB, Natowicz MR (August 2008). "Double outlet right ventricle: aetiologies and associations". J. Med. Genet. 45 (8): 481–97. doi:10.1136/jmg.2008.057984. PMID 18456715.
  2. 2.0 2.1 "Double outlet right ventricle : MedlinePlus Medical Encyclopedia". Archived from the original on 22 October 2021. Retrieved 27 October 2022.

External links

External resources