Absent pulmonary valve syndrome
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|Absent pulmonary valve syndrome|
|Other names: Congenital absence of the pulmonary valve|
|Prenatal ultrasonographic findings of absent pulmonary valve syndrome a) Marked dilatation of main and branch pulmonary arteries b-d) color and pulsed wave Doppler ultrasound shows to-and-fro pattern of pulmonary stenosis and regurgitation|
Absent pulmonary valve syndrome is a congenital heart defect that occurs when the flaps of the pulmonary valve do not develop. It presents at birth with breathing problems and a blue appearance.
There is (hypoplasia) resulting in aneurysms (dilation) of the pulmonary arteries and softening of the trachea and bronchi (tracheobronchomalacia).
It is frequently associated with ventricular septal defect, with around 3% to 6% having Tetralogy of Fallot.
- ↑ 1.0 1.1 1.2 "Absent pulmonary valve: MedlinePlus Medical Encyclopedia". medlineplus.gov. Archived from the original on 17 June 2022. Retrieved 27 October 2022.
- ↑ Ramaswamy, Prema (28 December 2020). "Tetralogy of Fallot With Absent Pulmonary Valve: Background, Pathophysiology, Etiology". Archived from the original on 31 August 2022. Retrieved 27 October 2022.