Epidermolysis bullosa pruriginosa

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Epidermolysis bullosa pruriginosa

Epidermolysis bullosa pruriginosa (EPB) is a type of dystrophic epidermolysis bullosa, belonging to the epidermolysis bullosa group of blistering conditions.[1] It may present in a young baby with blisters on the legs, or in young adults with itchy thick plaques.[1]

The condition runs in families, and arises from a mutation in the type II collagen gene.[1]

EPB is rare.[1] Less than 100 cases have been reported.[1] It was first reported in 1994.[1]

Signs and symptoms


  1. 1.0 1.1 1.2 1.3 1.4 1.5 Ball, Stephanie (2021). "Epidermolysis bullosa pruriginosa | DermNet". dermnetnz.org. Archived from the original on 21 February 2024. Retrieved 21 May 2024.