Cyanotic heart defect

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Cyanotic heart defect
Other names: Right-to-left circulatory shunt[1]

A cyanotic heart defect is any congenital heart defect (CHD) that occurs due to deoxygenated blood bypassing the lungs and entering the systemic circulation, or a mixture of oxygenated and unoxygenated blood entering the systemic circulation. It is caused by structural defects of the heart such as right-to-left or bidirectional shunting, malposition of the great arteries, or any condition which increases pulmonary vascular resistance. The result may be the development of collateral circulation.


Signs and symptoms

Presentation includes the following:[citation needed]

  • Clubbing
  • The patient assuming a crouching position
  • Cyanosis - bluish face, particularly the lips; and bluish fingers and toes
  • Crying
  • Crabbiness/irritability
  • Tachycardia
  • Tachypnea
  • A history of inadequate feeding
  • Unusually large toe and fingernails
  • Delayed development (both biological and physiological)


A neonate with a congenital cyanotic heart disease a)MRI shows a complete anomalous venous return b) T2-W coronal MRI shows a persistent left superior caval vein

The diagnosis for Cyanotic heart disease consist of the following:[3]


  • Morphine during Tet spells to decrease associated infundibular spasm.
  • Prophylactic: Propranolol/Inderall
  • Prostaglandin E (to keep the ductus arteriosus patent)
  • Prophylactic antibiotic to prevent endocarditis
  • Surgery: Variable. Superior Cavopulmonary Bypass (Bidirectional Glenn or Hemi-Fontan Procedure), Total Cavopulmonary Bypass (Fontan Completion Procedure). The purpose of these operations is to redirect the blood flow of the deoxygenated blood to the lungs by attaching the Vena Cava directly to the Pulmonary Artery causing the blood that flows into the lungs to be oxygenated before entering the chambers on the right side of the heart. Mathematical models are used to address the issue of pressure level alterations of circulation after the procedures. The pulmonary pressure resistance in the cavopulmonary connection is increased, and these models permit clear analyses of the pressure increase allowing doctors to avoid possible venous circulation congestion.

See also


  1. "Cyanotic heart disease: MedlinePlus Medical Encyclopedia". Archived from the original on 27 May 2019. Retrieved 27 May 2019.
  2. Page Elizabeth D Agabegi; Agabegi, Steven S. (2008). Step-Up to Medicine (Step-Up Series). Hagerstwon, MD: Lippincott Williams & Wilkins. ISBN 978-0-7817-7153-5.
  3. Ossa Galvis, Maria M.; Bhakta, Rupal T.; Tarmahomed, Abdulla; Mendez, Magda D. (2022). "Cyanotic Heart Disease". StatPearls. StatPearls Publishing. Archived from the original on 16 June 2022. Retrieved 12 August 2022.

External links

External resources