Carnitine O-palmitoyltransferase

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Choline/Carnitine o-acyltransferase
Structure of carnitine acetyltransferase.[1]
Identifiers
SymbolCarn_acyltransf
PfamPF00755
Pfam clanCL0149
InterProIPR000542
PROSITEPDOC00402
SCOP21ndi / SCOPe / SUPFAM
OPM superfamily83
OPM protein2h3u
Available protein structures:
Pfam  structures / ECOD  
PDBRCSB PDB; PDBe; PDBj
PDBsumstructure summary

Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme (EC 2.3.1.21) involved in the metabolism of palmitoylcarnitine into palmitoyl-CoA. A related transferase is carnitine acyltransferase.

Molecules

Pathway

Human forms

There are four different forms of CPT in humans:

See also

References

  1. ^ Jogl G, Tong L (January 2003). "Crystal structure of carnitine acetyltransferase and implications for the catalytic mechanism and fatty acid transport". Cell. 112 (1): 113–22. doi:10.1016/S0092-8674(02)01228-X. PMID 12526798.

External links