Adult cellular rhabdomyoma

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Adult cellular rhabdomyoma
Diagram showing common location of rhabdomyoma
ComplicationsAbnormal heart beat[1]
Usual onsetAdults >20-years[2]
Diagnostic methodEchocardiography[1]

Adult cellular rhabdomyoma (ACR), is a noncancerous primary tumor of the heart, similar to other adult skeletal muscle tumors outside the heart and distinct from cardiac rhabdomyoma.[1] It typically occurs in peopl older than 2-years of age.[2]

Unlike cardiac rhabdomyoma, adult cellular rhabdomyoma is not associated with any syndrome, and does not have the "spider cells" with vacuoles, which are characteristic of cardiac rhadomyoma.[2] ACRs appear well defined, of uniform tan color, and protrude into the chambers of the heart.[2]

It is rare and accounts or less than 2% of soft tissue tumors.[1]


  1. 1.0 1.1 1.2 1.3 WHO Classification of Tumours Editorial Board (2021). "3. Tumours of the heart: Adult cellular rhabdomyoma". Thoracic Tumours. Vol. 5 (5th ed.). Lyon (France): World Health Organization. pp. 241–242. ISBN 978-92-832-4506-3. Archived from the original on 2022-05-14. Retrieved 2022-07-26.
  2. 2.0 2.1 2.2 2.3 2.4 Maleszewski, Joseph J.; Basso, Cristina; Bois, Melanie C.; Glass, Carolyn; Klarich, Kyle W.; Leduc, Charles; Padera, Robert F.; Tavora, Fabio (April 2022). "The 2021 WHO Classification of Tumors of the Heart". Journal of Thoracic Oncology: Official Publication of the International Association for the Study of Lung Cancer. 17 (4): 510–518. doi:10.1016/j.jtho.2021.10.021. ISSN 1556-1380. PMID 34774791. Archived from the original on 2022-07-24. Retrieved 2022-07-26.